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2-Hydroxy-2-methylbutanoic acid - CAS 3739-30-8
2-Hydroxy-2-methylbutanoic acid - CAS 3739-30-8
SKU:MF-0005634-01
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Product Details
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Bioactivity
2-Hydroxy-2-methylbutyric acid is an unusual metabolite found in the urine of patients with 2-hydroxyglutaric aciduria and maple syrup urine disease.
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Target
Endogenous Metabolite
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Related Pathways
Metabolism
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CAS Number
3701
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Purity
0.9983
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Molecular Formula
C5H10O3
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Molecular Weight
118.13
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SMILES
CCC(C)(O)C(O)=O
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Storage Temperature
-20°C
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Shipping Conditions
Ice Packs
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Category
Natural Product