3-Amino-2-methylpropanoic acid - CAS 144-90-1

3-Amino-2-methylpropanoic acid (α-Methyl-β-alanine) is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6), the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.

Endogenous Metabolite

Metabolism

53

0.9943

C4H9NO2

103.12

CC(CN)C(O)=O

-20°C

Ice Packs

Natural Product