3-Methylglutaric acid - CAS 626-51-7

Methylglutaric acid is a leucine metabolite. A large amount of methylglutaric acid is identified in urine of patients with deficiency of 3-methylglutaconyl coenzyme A hydratase (PMID 6181239) . Methylglutaric acid is also found to be associated with 3-hydroxy-3-methylglutaryl-CoA lyase deficiency, another inborn error of metabolism.

Mitochondrial Metabolism, Endogenous Metabolite, ROS, ATPase

Membrane transporter/Ion channel, Immunology/Inflammation, Metabolism

568

0.9953

C6H10O4

146.14

C(C(CC(O)=O)C)C(O)=O

-20°C

Ice Packs

Natural Product